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Applicable To Crosswalk
Code Also Crosswalk
Code First Crosswalk
Includes Crosswalk
Note Crosswalk
Type 1 Excludes Crosswalk
Type 2 Excludes Crosswalk
Use Additional Crosswalk
Changes
ICD-10-CM
New 2020 Codes
Codes Revised in 2020
Codes Deleted in 2020
ICD-10-PCS
New 2020 Codes
Codes Revised in 2020
Codes Deleted in 2020
Index Terms Starting With 'D' (Deficiency, deficient)
2021 ICD-10-CM Index
›
'D' Terms
›
Index Terms Starting With 'D' (Deficiency, deficient)
Index Terms Starting With 'D' (Deficiency, deficient)
Deficiency, deficient
11-hydroxylase
E25.0
ICD-10-CM Diagnosis Code
E25.0
Congenital adrenogenital disorders associated with enzyme deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Congenital adrenal hyperplasia
21-Hydroxylase deficiency
Salt-losing congenital adrenal hyperplasia
21-hydroxylase
E25.0
ICD-10-CM Diagnosis Code
E25.0
Congenital adrenogenital disorders associated with enzyme deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Congenital adrenal hyperplasia
21-Hydroxylase deficiency
Salt-losing congenital adrenal hyperplasia
3-beta hydroxysteroid dehydrogenase
E25.0
ICD-10-CM Diagnosis Code
E25.0
Congenital adrenogenital disorders associated with enzyme deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Congenital adrenal hyperplasia
21-Hydroxylase deficiency
Salt-losing congenital adrenal hyperplasia
5-alpha reductase
E29.1
(with male pseudohermaphroditism)
ICD-10-CM Diagnosis Code
E29.1
Testicular hypofunction
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Male Dx
Applicable To
Defective biosynthesis of testicular androgen NOS
5-delta-Reductase deficiency (with male pseudohermaphroditism)
Testicular hypogonadism NOS
Type 1 Excludes
postprocedural testicular hypofunction (
E89.5
)
Use Additional
code for adverse effect, if applicable, to identify drug (
T36-T50
with fifth or sixth character 5)
AADC
E70.81
(aromatic L-amino acid decarboxylase)
ICD-10-CM Diagnosis Code
E70.81
Aromatic L-amino acid decarboxylase deficiency
2021 - New Code
Billable/Specific Code
Applicable To
AADC deficiency
abdominal muscle syndrome
Q79.4
ICD-10-CM Diagnosis Code
Q79.4
Prune belly syndrome
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
Applicable To
Congenital prolapse of bladder mucosa
Eagle-Barrett syndrome
AC globulin (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
accelerator globulin
D68.2
(Ac G) (blood)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acid phosphatase
E83.39
ICD-10-CM Diagnosis Code
E83.39
Other disorders of phosphorus metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Acid phosphatase deficiency
Hypophosphatasia
activating factor
D68.2
(blood)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
ADA2
D81.32
(adenosine deaminase 2)
ICD-10-CM Diagnosis Code
D81.32
Adenosine deaminase 2 deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
ADA2 deficiency
Adenosine deaminase deficiency type 2
Code Also
, if applicable, any associated manifestations, such as:
polyarteritis nodosa (
M30.0
)
stroke (
I63.-
)
adenosine deaminase (ADA)
D81.30
ICD-10-CM Diagnosis Code
D81.30
Adenosine deaminase deficiency, unspecified
2020 - New Code
2021
Billable/Specific Code
Applicable To
ADA deficiency NOS
partial
D81.39
(type 1)
ICD-10-CM Diagnosis Code
D81.39
Other adenosine deaminase deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
Adenosine deaminase [ADA] deficiency type 1, NOS
Adenosine deaminase [ADA] deficiency type 1, without SCID
Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
Partial ADA deficiency (type 1)
Partial adenosine deaminase deficiency (type 1)
specified NEC
D81.39
ICD-10-CM Diagnosis Code
D81.39
Other adenosine deaminase deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
Adenosine deaminase [ADA] deficiency type 1, NOS
Adenosine deaminase [ADA] deficiency type 1, without SCID
Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
Partial ADA deficiency (type 1)
Partial adenosine deaminase deficiency (type 1)
type 1
D81.39
(without SCID) (without severe combined immunodeficiency)
ICD-10-CM Diagnosis Code
D81.39
Other adenosine deaminase deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
Adenosine deaminase [ADA] deficiency type 1, NOS
Adenosine deaminase [ADA] deficiency type 1, without SCID
Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
Partial ADA deficiency (type 1)
Partial adenosine deaminase deficiency (type 1)
type 2
D81.32
ICD-10-CM Diagnosis Code
D81.32
Adenosine deaminase 2 deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
ADA2 deficiency
Adenosine deaminase deficiency type 2
Code Also
, if applicable, any associated manifestations, such as:
polyarteritis nodosa (
M30.0
)
stroke (
I63.-
)
with severe combined immunodeficiency
D81.31
(SCID)
ICD-10-CM Diagnosis Code
D81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
2020 - New Code
2021
Billable/Specific Code
Applicable To
ADA deficiency with SCID
Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency
aldolase
E74.19
(hereditary)
ICD-10-CM Diagnosis Code
E74.19
Other disorders of fructose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fructose-1, 6-diphosphatase deficiency
alpha-1-antitrypsin
E88.01
ICD-10-CM Diagnosis Code
E88.01
Alpha-1-antitrypsin deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AAT deficiency
amino-acids
E72.9
ICD-10-CM Diagnosis Code
E72.9
Disorder of amino-acid metabolism, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
anemia - see
Anemia
aneurin
E51.9
ICD-10-CM Diagnosis Code
E51.9
Thiamine deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
anti-hemophilic
factor (A)
D66
ICD-10-CM Diagnosis Code
D66
Hereditary factor VIII deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A
Type 1 Excludes
factor VIII deficiency with vascular defect (
D68.0
)
B
D67
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
C
D68.1
ICD-10-CM Diagnosis Code
D68.1
Hereditary factor XI deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
globulin
D66
(AHG)
ICD-10-CM Diagnosis Code
D66
Hereditary factor VIII deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A
Type 1 Excludes
factor VIII deficiency with vascular defect (
D68.0
)
antibody with
hyperimmunoglobulinemia
D80.6
ICD-10-CM Diagnosis Code
D80.6
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
near-normal immunoglobins
D80.6
ICD-10-CM Diagnosis Code
D80.6
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
antidiuretic hormone
E23.2
ICD-10-CM Diagnosis Code
E23.2
Diabetes insipidus
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
nephrogenic diabetes insipidus (
N25.1
)
antithrombin
D68.59
(antithrombin III)
ICD-10-CM Diagnosis Code
D68.59
Other primary thrombophilia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Antithrombin III deficiency
Hypercoagulable state NOS
Primary hypercoagulable state NEC
Primary thrombophilia NEC
Protein C deficiency
Protein S deficiency
Thrombophilia NOS
aromatic L-amino acid decarboxylase
E70.81
(AADC)
ICD-10-CM Diagnosis Code
E70.81
Aromatic L-amino acid decarboxylase deficiency
2021 - New Code
Billable/Specific Code
Applicable To
AADC deficiency
ascorbic acid
E54
ICD-10-CM Diagnosis Code
E54
Ascorbic acid deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of vitamin C
Scurvy
Type 1 Excludes
scorbutic anemia (
D53.2
)
sequelae of vitamin C deficiency (
E64.2
)
attention (disorder) (syndrome)
F98.8
ICD-10-CM Diagnosis Code
F98.8
Other specified behavioral and emotional disorders with onset usually occurring in childhood and adolescence
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Excessive masturbation
Nail-biting
Nose-picking
Thumb-sucking
with hyperactivity - see
Disorder, attention-deficit hyperactivity
autoprothrombin
C
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
I
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
II
D67
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
beta-glucuronidase
E76.29
ICD-10-CM Diagnosis Code
E76.29
Other mucopolysaccharidoses
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
beta-Glucuronidase deficiency
Maroteaux-Lamy (mild) (severe) syndrome
Mucopolysaccharidosis, types VI, VII
biotin
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
biotin-dependent carboxylase
D81.819
ICD-10-CM Diagnosis Code
D81.819
Biotin-dependent carboxylase deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Multiple carboxylase deficiency, unspecified
biotinidase
D81.810
ICD-10-CM Diagnosis Code
D81.810
Biotinidase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
brancher enzyme
E74.03
(amylopectinosis)
ICD-10-CM Diagnosis Code
E74.03
Cori disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Forbes disease
Type III glycogen storage disease
C1 esterase inhibitor
D84.1
(C1-INH)
ICD-10-CM Diagnosis Code
D84.1
Defects in the complement system
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
C1 esterase inhibitor [C1-INH] deficiency
calciferol
E55.9
ICD-10-CM Diagnosis Code
E55.9
Vitamin D deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Avitaminosis D
with
adult osteomalacia
M83.8
ICD-10-CM Diagnosis Code
M83.8
Other adult osteomalacia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Adult Dx (15-124 years)
rickets - see
Rickets
calcium
E58
(dietary)
ICD-10-CM Diagnosis Code
E58
Dietary calcium deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
disorders of calcium metabolism (
E83.5-
)
sequelae of calcium deficiency (
E64.8
)
calorie, severe
E43
ICD-10-CM Diagnosis Code
E43
Unspecified severe protein-calorie malnutrition
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Starvation edema
with marasmus
E41
ICD-10-CM Diagnosis Code
E41
Nutritional marasmus
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Severe malnutrition with marasmus
Type 1 Excludes
marasmic kwashiorkor (
E42
)
and kwashiorkor
E42
ICD-10-CM Diagnosis Code
E42
Marasmic kwashiorkor
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Intermediate form severe protein-calorie malnutrition
Severe protein-calorie malnutrition with signs of both kwashiorkor and marasmus
cardiac - see
Insufficiency, myocardial
carnitine
E71.40
ICD-10-CM Diagnosis Code
E71.40
Disorder of carnitine metabolism, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
due to
hemodialysis
E71.43
ICD-10-CM Diagnosis Code
E71.43
Iatrogenic carnitine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Carnitine deficiency due to hemodialysis
Carnitine deficiency due to Valproic acid therapy
inborn errors of metabolism
E71.42
ICD-10-CM Diagnosis Code
E71.42
Carnitine deficiency due to inborn errors of metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code Also
associated inborn error or metabolism
Valproic acid therapy
E71.43
ICD-10-CM Diagnosis Code
E71.43
Iatrogenic carnitine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Carnitine deficiency due to hemodialysis
Carnitine deficiency due to Valproic acid therapy
iatrogenic
E71.43
ICD-10-CM Diagnosis Code
E71.43
Iatrogenic carnitine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Carnitine deficiency due to hemodialysis
Carnitine deficiency due to Valproic acid therapy
muscle palmityltransferase
E71.314
ICD-10-CM Diagnosis Code
E71.314
Muscle carnitine palmitoyltransferase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
primary
E71.41
ICD-10-CM Diagnosis Code
E71.41
Primary carnitine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
secondary
E71.448
ICD-10-CM Diagnosis Code
E71.448
Other secondary carnitine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
carotene
E50.9
ICD-10-CM Diagnosis Code
E50.9
Vitamin A deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hypovitaminosis A NOS
central nervous system
G96.89
ICD-10-CM Diagnosis Code
G96.89
Other specified disorders of central nervous system
2021 - New Code
Billable/Specific Code
ceruloplasmin
E83.01
(Wilson)
ICD-10-CM Diagnosis Code
E83.01
Wilson's disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code Also
associated Kayser Fleischer ring (
H18.04-
)
choline
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
Christmas factor
D67
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
chromium
E61.4
ICD-10-CM Diagnosis Code
E61.4
Chromium deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
clotting
D68.9
(blood) - see also
Deficiency, coagulation factor
ICD-10-CM Diagnosis Code
D68.9
Coagulation defect, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
clotting factor NEC
D68.2
(hereditary) - see also
Deficiency, factor
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
coagulation NOS
D68.9
ICD-10-CM Diagnosis Code
D68.9
Coagulation defect, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
acquired
D68.4
(any)
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
antepartum hemorrhage - see
Hemorrhage, antepartum, with coagulation defect
clotting factor NEC
D68.2
- see also
Deficiency, factor
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
due to
hyperprothrombinemia
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
liver disease
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
vitamin K deficiency
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
newborn, transient
P61.6
ICD-10-CM Diagnosis Code
P61.6
Other transient neonatal disorders of coagulation
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code on Newborn Record
postpartum
O72.3
ICD-10-CM Diagnosis Code
O72.3
Postpartum coagulation defects
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Maternity Dx (12-55 years)
Applicable To
Postpartum afibrinogenemia
Postpartum fibrinolysis
specified NEC
D68.8
ICD-10-CM Diagnosis Code
D68.8
Other specified coagulation defects
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
hemorrhagic disease of newborn (
P53
)
with
ectopic pregnancy
O08.1
ICD-10-CM Diagnosis Code
O08.1
Delayed or excessive hemorrhage following ectopic and molar pregnancy
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Maternity Dx (12-55 years)
Applicable To
Afibrinogenemia following ectopic and molar pregnancy
Defibrination syndrome following ectopic and molar pregnancy
Hemolysis following ectopic and molar pregnancy
Intravascular coagulation following ectopic and molar pregnancy
Type 1 Excludes
delayed or excessive hemorrhage due to incomplete abortion (
O03.1
)
molar pregnancy
O08.1
ICD-10-CM Diagnosis Code
O08.1
Delayed or excessive hemorrhage following ectopic and molar pregnancy
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Maternity Dx (12-55 years)
Applicable To
Afibrinogenemia following ectopic and molar pregnancy
Defibrination syndrome following ectopic and molar pregnancy
Hemolysis following ectopic and molar pregnancy
Intravascular coagulation following ectopic and molar pregnancy
Type 1 Excludes
delayed or excessive hemorrhage due to incomplete abortion (
O03.1
)
cognitive
F09
ICD-10-CM Diagnosis Code
F09
Unspecified mental disorder due to known physiological condition
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Mental disorder NOS due to known physiological condition
Organic brain syndrome NOS
Organic mental disorder NOS
Organic psychosis NOS
Symptomatic psychosis NOS
Code First
the underlying physiological condition
Type 1 Excludes
psychosis NOS (
F29
)
color vision
H53.50
ICD-10-CM Diagnosis Code
H53.50
Unspecified color vision deficiencies
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Color blindness NOS
achromatopsia
H53.51
ICD-10-CM Diagnosis Code
H53.51
Achromatopsia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
acquired
H53.52
ICD-10-CM Diagnosis Code
H53.52
Acquired color vision deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
deuteranomaly
H53.53
ICD-10-CM Diagnosis Code
H53.53
Deuteranomaly
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deuteranopia
protanomaly
H53.54
ICD-10-CM Diagnosis Code
H53.54
Protanomaly
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Protanopia
specified type NEC
H53.59
ICD-10-CM Diagnosis Code
H53.59
Other color vision deficiencies
2016
2017
2018
2019
2020
2021
Billable/Specific Code
tritanomaly
H53.55
ICD-10-CM Diagnosis Code
H53.55
Tritanomaly
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Tritanopia
combined glucocorticoid and mineralocorticoid
E27.49
ICD-10-CM Diagnosis Code
E27.49
Other adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenal hemorrhage
Adrenal infarction
contact factor
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
copper
E61.0
(nutritional)
ICD-10-CM Diagnosis Code
E61.0
Copper deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
corticoadrenal
E27.40
ICD-10-CM Diagnosis Code
E27.40
Unspecified adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenocortical insufficiency NOS
Hypoaldosteronism
primary
E27.1
ICD-10-CM Diagnosis Code
E27.1
Primary adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Addison's disease
Autoimmune adrenalitis
Type 1 Excludes
Addison only phenotype adrenoleukodystrophy (
E71.528
)
amyloidosis (
E85.-
)
tuberculous Addison's disease (
A18.7
)
Waterhouse-Friderichsen syndrome (
A39.1
)
craniofacial axis
Q75.0
ICD-10-CM Diagnosis Code
Q75.0
Craniosynostosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
Applicable To
Acrocephaly
Imperfect fusion of skull
Oxycephaly
Trigonocephaly
cyanocobalamin
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
debrancher enzyme
E74.03
(limit dextrinosis)
ICD-10-CM Diagnosis Code
E74.03
Cori disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Forbes disease
Type III glycogen storage disease
dehydrogenase
long chain/very long chain acyl CoA
E71.310
ICD-10-CM Diagnosis Code
E71.310
Long chain/very long chain acyl CoA dehydrogenase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
LCAD
VLCAD
medium chain acyl CoA
E71.311
ICD-10-CM Diagnosis Code
E71.311
Medium chain acyl CoA dehydrogenase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
MCAD
short chain acyl CoA
E71.312
ICD-10-CM Diagnosis Code
E71.312
Short chain acyl CoA dehydrogenase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
SCAD
diet
E63.9
ICD-10-CM Diagnosis Code
E63.9
Nutritional deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
dihydropyrimidine dehydrogenase
E88.89
(DPD)
ICD-10-CM Diagnosis Code
E88.89
Other specified metabolic disorders
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Launois-Bensaude adenolipomatosis
Type 1 Excludes
adult pulmonary Langerhans cell histiocytosis (
J84.82
)
disaccharidase
E73.9
ICD-10-CM Diagnosis Code
E73.9
Lactose intolerance, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
edema - see
Malnutrition, severe
endocrine
E34.9
ICD-10-CM Diagnosis Code
E34.9
Endocrine disorder, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Endocrine disturbance NOS
Hormone disturbance NOS
energy-supply - see
Malnutrition
enzymes, circulating NEC
E88.09
ICD-10-CM Diagnosis Code
E88.09
Other disorders of plasma-protein metabolism, not elsewhere classified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bisalbuminemia
ergosterol
E55.9
ICD-10-CM Diagnosis Code
E55.9
Vitamin D deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Avitaminosis D
with
adult osteomalacia
M83.8
ICD-10-CM Diagnosis Code
M83.8
Other adult osteomalacia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Adult Dx (15-124 years)
rickets - see
Rickets
essential fatty acid
E63.0
(EFA)
ICD-10-CM Diagnosis Code
E63.0
Essential fatty acid [EFA] deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
eye movements
saccadic
H55.81
ICD-10-CM Diagnosis Code
H55.81
Deficient saccadic eye movements
2016
2017
2018
2019
2020
2021 - Revised Code
Billable/Specific Code
smooth pursuit
H55.82
ICD-10-CM Diagnosis Code
H55.82
Deficient smooth pursuit eye movements
2021 - New Code
Billable/Specific Code
factor - see also
Deficiency, coagulation
Hageman
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
I
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
II
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
IX
D67
(congenital) (functional) (hereditary) (with functional defect)
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
multiple (congenital)
D68.8
ICD-10-CM Diagnosis Code
D68.8
Other specified coagulation defects
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
hemorrhagic disease of newborn (
P53
)
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
V
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
VII
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
VIII (congenital) (functional) (hereditary) (with functional defect)
D66
ICD-10-CM Diagnosis Code
D66
Hereditary factor VIII deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A
Type 1 Excludes
factor VIII deficiency with vascular defect (
D68.0
)
with vascular defect
D68.0
ICD-10-CM Diagnosis Code
D68.0
Von Willebrand's disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Angiohemophilia
Factor VIII deficiency with vascular defect
Vascular hemophilia
Type 1 Excludes
capillary fragility (hereditary) (
D69.8
)
factor VIII deficiency NOS (
D66
)
factor VIII deficiency with functional defect (
D66
)
X
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
XI
D68.1
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.1
Hereditary factor XI deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
XII
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
XIII
D68.2
(congenital) (hereditary)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
femoral, proximal focal (congenital) - see
Defect, reduction, lower limb, longitudinal, femur
fibrin-stabilizing factor (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
fibrinase
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
fibrinogen (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D65
ICD-10-CM Diagnosis Code
D65
Disseminated intravascular coagulation [defibrination syndrome]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Afibrinogenemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic hemorrhage, acquired
Fibrinolytic purpura
Purpura fulminans
Type 1 Excludes
disseminated intravascular coagulation (complicating):
abortion or ectopic or molar pregnancy (
O00
-
O07
,
O08.1
)
in newborn (
P60
)
pregnancy, childbirth and the puerperium (
O45.0
,
O46.0
,
O67.0
,
O72.3
)
folate
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
folic acid
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
foreskin
N47.3
ICD-10-CM Diagnosis Code
N47.3
Deficient foreskin
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Male Dx
fructokinase
E74.11
ICD-10-CM Diagnosis Code
E74.11
Essential fructosuria
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fructokinase deficiency
fructose 1,6-diphosphatase
E74.19
ICD-10-CM Diagnosis Code
E74.19
Other disorders of fructose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fructose-1, 6-diphosphatase deficiency
fructose-1-phosphate aldolase
E74.19
ICD-10-CM Diagnosis Code
E74.19
Other disorders of fructose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fructose-1, 6-diphosphatase deficiency
GABA
E72.81
(gamma aminobutyric acid)
ICD-10-CM Diagnosis Code
E72.81
Disorders of gamma aminobutyric acid metabolism
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
4-hydroxybutyric aciduria
Disorders of GABA metabolism
GABA metabolic defect
GABA transaminase deficiency
GABA-T deficiency
Gamma-hydroxybutyric aciduria
SSADHD
Succinic semialdehyde dehydrogenase deficiency
GABA-T
E72.81
(gamma aminobutyric acid transaminase)
ICD-10-CM Diagnosis Code
E72.81
Disorders of gamma aminobutyric acid metabolism
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
4-hydroxybutyric aciduria
Disorders of GABA metabolism
GABA metabolic defect
GABA transaminase deficiency
GABA-T deficiency
Gamma-hydroxybutyric aciduria
SSADHD
Succinic semialdehyde dehydrogenase deficiency
galactokinase
E74.29
ICD-10-CM Diagnosis Code
E74.29
Other disorders of galactose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Galactokinase deficiency
galactose-1-phosphate uridyl transferase
E74.29
ICD-10-CM Diagnosis Code
E74.29
Other disorders of galactose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Galactokinase deficiency
gammaglobulin in blood
D80.1
ICD-10-CM Diagnosis Code
D80.1
Nonfamilial hypogammaglobulinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinemia [CVAgamma]
Hypogammaglobulinemia NOS
hereditary
D80.0
ICD-10-CM Diagnosis Code
D80.0
Hereditary hypogammaglobulinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Autosomal recessive agammaglobulinemia (Swiss type)
X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
glass factor
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
glucocorticoid
E27.49
ICD-10-CM Diagnosis Code
E27.49
Other adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenal hemorrhage
Adrenal infarction
mineralocorticoid
E27.49
ICD-10-CM Diagnosis Code
E27.49
Other adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenal hemorrhage
Adrenal infarction
glucose transporter protein type 1
E74.810
ICD-10-CM Diagnosis Code
E74.810
Glucose transporter protein type 1 deficiency
2021 - New Code
Billable/Specific Code
Applicable To
De Vivo syndrome
Glucose transport defect, blood-brain barrier
Glut1 deficiency
GLUT1 deficiency syndrome 1, infantile onset
GLUT1 deficiency syndrome 2, childhood onset
glucose-6-phosphatase
E74.01
ICD-10-CM Diagnosis Code
E74.01
von Gierke disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Type I glycogen storage disease
glucose-6-phosphate dehydrogenase
anemia
D55.0
ICD-10-CM Diagnosis Code
D55.0
Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Favism
G6PD deficiency anemia
Type 1 Excludes
glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (
D75.A
)
without anemia
D75.A
ICD-10-CM Diagnosis Code
D75.A
Glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia
2020 - New Code
2021
Billable/Specific Code
Type 1 Excludes
glucose-6-phosphate dehydrogenase (G6PD) deficiency with anemia (
D55.0
)
glucuronyl transferase
E80.5
ICD-10-CM Diagnosis Code
E80.5
Crigler-Najjar syndrome
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Glut1
E74.810
ICD-10-CM Diagnosis Code
E74.810
Glucose transporter protein type 1 deficiency
2021 - New Code
Billable/Specific Code
Applicable To
De Vivo syndrome
Glucose transport defect, blood-brain barrier
Glut1 deficiency
GLUT1 deficiency syndrome 1, infantile onset
GLUT1 deficiency syndrome 2, childhood onset
glycogen synthetase
E74.09
ICD-10-CM Diagnosis Code
E74.09
Other glycogen storage disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
gonadotropin
E23.0
(isolated)
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
growth hormone
E23.0
(idiopathic) (isolated)
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
Hageman factor
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
hemoglobin
D64.9
ICD-10-CM Diagnosis Code
D64.9
Anemia, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
hepatophosphorylase
E74.09
ICD-10-CM Diagnosis Code
E74.09
Other glycogen storage disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
homogentisate 1,2-dioxygenase
E70.29
ICD-10-CM Diagnosis Code
E70.29
Other disorders of tyrosine metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Alkaptonuria
Ochronosis
hormone
anterior pituitary (partial)
E23.0
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
growth
E23.0
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
growth
E23.0
(isolated)
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
pituitary
E23.0
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
testicular
E29.1
ICD-10-CM Diagnosis Code
E29.1
Testicular hypofunction
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Male Dx
Applicable To
Defective biosynthesis of testicular androgen NOS
5-delta-Reductase deficiency (with male pseudohermaphroditism)
Testicular hypogonadism NOS
Type 1 Excludes
postprocedural testicular hypofunction (
E89.5
)
Use Additional
code for adverse effect, if applicable, to identify drug (
T36-T50
with fifth or sixth character 5)
hypoxanthine-
E79.1
(guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)
ICD-10-CM Diagnosis Code
E79.1
Lesch-Nyhan syndrome
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
HGPRT deficiency
immunity
D84.9
ICD-10-CM Diagnosis Code
D84.9
Immunodeficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Immunocompromised NOS
Immunodeficient NOS
Immunosuppressed NOS
cell-mediated
D84.89
ICD-10-CM Diagnosis Code
D84.89
Other immunodeficiencies
2021 - New Code
Billable/Specific Code
with thrombocytopenia and eczema
D82.0
ICD-10-CM Diagnosis Code
D82.0
Wiskott-Aldrich syndrome
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Immunodeficiency with thrombocytopenia and eczema
combined
D81.9
ICD-10-CM Diagnosis Code
D81.9
Combined immunodeficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Severe combined immunodeficiency disorder [SCID] NOS
humoral
D80.9
ICD-10-CM Diagnosis Code
D80.9
Immunodeficiency with predominantly antibody defects, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
IgA
D80.2
(secretory)
ICD-10-CM Diagnosis Code
D80.2
Selective deficiency of immunoglobulin A [IgA]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
IgG
D80.3
ICD-10-CM Diagnosis Code
D80.3
Selective deficiency of immunoglobulin G [IgG] subclasses
2016
2017
2018
2019
2020
2021
Billable/Specific Code
IgM
D80.4
ICD-10-CM Diagnosis Code
D80.4
Selective deficiency of immunoglobulin M [IgM]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
immuno - see
Immunodeficiency
immunoglobulin, selective
A
D80.2
(IgA)
ICD-10-CM Diagnosis Code
D80.2
Selective deficiency of immunoglobulin A [IgA]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
G
D80.3
(IgG) (subclasses)
ICD-10-CM Diagnosis Code
D80.3
Selective deficiency of immunoglobulin G [IgG] subclasses
2016
2017
2018
2019
2020
2021
Billable/Specific Code
M
D80.4
(IgM)
ICD-10-CM Diagnosis Code
D80.4
Selective deficiency of immunoglobulin M [IgM]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
inositol
E53.8
(B complex)
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
intrinsic
factor
D51.0
(congenital)
ICD-10-CM Diagnosis Code
D51.0
Vitamin B12 deficiency anemia due to intrinsic factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Addison anemia
Biermer anemia
Pernicious (congenital) anemia
Congenital intrinsic factor deficiency
sphincter
N36.42
ICD-10-CM Diagnosis Code
N36.42
Intrinsic sphincter deficiency (ISD)
2016
2017
2018
2019
2020
2021
Billable/Specific Code
with urethral hypermobility
N36.43
ICD-10-CM Diagnosis Code
N36.43
Combined hypermobility of urethra and intrinsic sphincter deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
iodine
E61.8
ICD-10-CM Diagnosis Code
E61.8
Deficiency of other specified nutrient elements
2016
2017
2018
2019
2020
2021
Billable/Specific Code
congenital syndrome - see
Syndrome, iodine-deficiency, congenital
iron
E61.1
ICD-10-CM Diagnosis Code
E61.1
Iron deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
iron deficiency anemia (
D50.-
)
anemia
D50.9
ICD-10-CM Diagnosis Code
D50.9
Iron deficiency anemia, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
kalium
E87.6
ICD-10-CM Diagnosis Code
E87.6
Hypokalemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Potassium [K] deficiency
kappa-light chain
D80.8
ICD-10-CM Diagnosis Code
D80.8
Other immunodeficiencies with predominantly antibody defects
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Kappa light chain deficiency
labile factor (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
lacrimal fluid (acquired) - see also
Syndrome, dry eye
congenital
Q10.6
ICD-10-CM Diagnosis Code
Q10.6
Other congenital malformations of lacrimal apparatus
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
Applicable To
Congenital malformation of lacrimal apparatus NOS
lactase
congenital
E73.0
ICD-10-CM Diagnosis Code
E73.0
Congenital lactase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
secondary
E73.1
ICD-10-CM Diagnosis Code
E73.1
Secondary lactase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Laki-Lorand factor
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
lecithin cholesterol acyltransferase
E78.6
ICD-10-CM Diagnosis Code
E78.6
Lipoprotein deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Abetalipoproteinemia
Depressed HDL cholesterol
High-density lipoprotein deficiency
Hypoalphalipoproteinemia
Hypobetalipoproteinemia (familial)
Lecithin cholesterol acyltransferase deficiency
Tangier disease
lipocaic
K86.89
ICD-10-CM Diagnosis Code
K86.89
Other specified diseases of pancreas
2017 - New Code
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Aseptic pancreatic necrosis, unrelated to acute pancreatitis
Atrophy of pancreas
Calculus of pancreas
Cirrhosis of pancreas
Fibrosis of pancreas
Pancreatic fat necrosis, unrelated to acute pancreatitis
Pancreatic infantilism
Pancreatic necrosis NOS, unrelated to acute pancreatitis
lipoprotein
E78.6
(familial) (high density)
ICD-10-CM Diagnosis Code
E78.6
Lipoprotein deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Abetalipoproteinemia
Depressed HDL cholesterol
High-density lipoprotein deficiency
Hypoalphalipoproteinemia
Hypobetalipoproteinemia (familial)
Lecithin cholesterol acyltransferase deficiency
Tangier disease
liver phosphorylase
E74.09
ICD-10-CM Diagnosis Code
E74.09
Other glycogen storage disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
lysosomal alpha-1, 4 glucosidase
E74.02
ICD-10-CM Diagnosis Code
E74.02
Pompe disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Cardiac glycogenosis
Type II glycogen storage disease
magnesium
E61.2
ICD-10-CM Diagnosis Code
E61.2
Magnesium deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
major histocompatibility complex
class I
D81.6
ICD-10-CM Diagnosis Code
D81.6
Major histocompatibility complex class I deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bare lymphocyte syndrome
class II
D81.7
ICD-10-CM Diagnosis Code
D81.7
Major histocompatibility complex class II deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
manganese
E61.3
ICD-10-CM Diagnosis Code
E61.3
Manganese deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
menadione (vitamin K)
E56.1
ICD-10-CM Diagnosis Code
E56.1
Deficiency of vitamin K
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
deficiency of coagulation factor due to vitamin K deficiency (
D68.4
)
vitamin K deficiency of newborn (
P53
)
newborn
P53
ICD-10-CM Diagnosis Code
P53
Hemorrhagic disease of newborn
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code on Newborn Record
Applicable To
Vitamin K deficiency of newborn
mental (familial) (hereditary) - see
Disability, intellectual
methylenetetrahydrofolate reductase
E72.12
(MTHFR)
ICD-10-CM Diagnosis Code
E72.12
Methylenetetrahydrofolate reductase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
mevalonate kinase
M04.1
ICD-10-CM Diagnosis Code
M04.1
Periodic fever syndromes
2017 - New Code
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Familial Mediterranean fever
Hyperimmunoglobin D syndrome
Mevalonate kinase deficiency
Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
mineral NEC
E61.8
ICD-10-CM Diagnosis Code
E61.8
Deficiency of other specified nutrient elements
2016
2017
2018
2019
2020
2021
Billable/Specific Code
mineralocorticoid
E27.49
ICD-10-CM Diagnosis Code
E27.49
Other adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenal hemorrhage
Adrenal infarction
with glucocorticoid
E27.49
ICD-10-CM Diagnosis Code
E27.49
Other adrenocortical insufficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Adrenal hemorrhage
Adrenal infarction
molybdenum
E61.5
(nutritional)
ICD-10-CM Diagnosis Code
E61.5
Molybdenum deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
moral
F60.2
ICD-10-CM Diagnosis Code
F60.2
Antisocial personality disorder
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Amoral personality (disorder)
Asocial personality (disorder)
Dissocial personality disorder
Psychopathic personality (disorder)
Sociopathic personality (disorder)
Type 1 Excludes
conduct disorders (
F91.-
)
Type 2 Excludes
borderline personality disorder (
F60.3
)
multiple nutrient elements
E61.7
ICD-10-CM Diagnosis Code
E61.7
Deficiency of multiple nutrient elements
2016
2017
2018
2019
2020
2021
Billable/Specific Code
multiple sulfatase
E75.26
(MSD)
ICD-10-CM Diagnosis Code
E75.26
Sulfatase deficiency
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
Multiple sulfatase deficiency (MSD)
muscle
carnitine
E71.314
(palmityltransferase)
ICD-10-CM Diagnosis Code
E71.314
Muscle carnitine palmitoyltransferase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
phosphofructokinase
E74.09
ICD-10-CM Diagnosis Code
E74.09
Other glycogen storage disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
myoadenylate deaminase
E79.2
ICD-10-CM Diagnosis Code
E79.2
Myoadenylate deaminase deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
myocardial - see
Insufficiency, myocardial
myophosphorylase
E74.04
ICD-10-CM Diagnosis Code
E74.04
McArdle disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Type V glycogen storage disease
NADH diaphorase or reductase
D74.0
(congenital)
ICD-10-CM Diagnosis Code
D74.0
Congenital methemoglobinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Congenital NADH-methemoglobin reductase deficiency
Hemoglobin-M [Hb-M] disease
Methemoglobinemia, hereditary
NADH-methemoglobin reductase
D74.0
(congenital)
ICD-10-CM Diagnosis Code
D74.0
Congenital methemoglobinemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Congenital NADH-methemoglobin reductase deficiency
Hemoglobin-M [Hb-M] disease
Methemoglobinemia, hereditary
natrium
E87.1
ICD-10-CM Diagnosis Code
E87.1
Hypo-osmolality and hyponatremia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Sodium [Na] deficiency
Type 1 Excludes
syndrome of inappropriate secretion of antidiuretic hormone (
E22.2
)
niacin
E52
(amide) (-tryptophan)
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
nicotinamide
E52
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
nicotinic acid
E52
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
number of teeth - see
Anodontia
nutrient element
E61.9
ICD-10-CM Diagnosis Code
E61.9
Deficiency of nutrient element, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
multiple
E61.7
ICD-10-CM Diagnosis Code
E61.7
Deficiency of multiple nutrient elements
2016
2017
2018
2019
2020
2021
Billable/Specific Code
specified NEC
E61.8
ICD-10-CM Diagnosis Code
E61.8
Deficiency of other specified nutrient elements
2016
2017
2018
2019
2020
2021
Billable/Specific Code
nutrition, nutritional
E63.9
ICD-10-CM Diagnosis Code
E63.9
Nutritional deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
sequelae - see
Sequelae, nutritional deficiency
specified NEC
E63.8
ICD-10-CM Diagnosis Code
E63.8
Other specified nutritional deficiencies
2016
2017
2018
2019
2020
2021
Billable/Specific Code
of interleukin 1 receptor antagonist [DIRA]
M04.8
ICD-10-CM Diagnosis Code
M04.8
Other autoinflammatory syndromes
2017 - New Code
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Blau syndrome
Deficiency of interleukin 1 receptor antagonist [DIRA]
Majeed syndrome
Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
ornithine transcarbamylase
E72.4
ICD-10-CM Diagnosis Code
E72.4
Disorders of ornithine metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
Ornithinemia (types I, II)
Ornithine transcarbamylase deficiency
Type 1 Excludes
hereditary choroidal dystrophy (
H31.2-
)
ovarian
E28.39
ICD-10-CM Diagnosis Code
E28.39
Other primary ovarian failure
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Decreased estrogen
Resistant ovary syndrome
oxygen - see
Anoxia
pantothenic acid
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
parathyroid
E20.9
(gland)
ICD-10-CM Diagnosis Code
E20.9
Hypoparathyroidism, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Parathyroid tetany
perineum
N81.89
(female)
ICD-10-CM Diagnosis Code
N81.89
Other female genital prolapse
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficient perineum
Old laceration of muscles of pelvic floor
phenylalanine hydroxylase
E70.1
ICD-10-CM Diagnosis Code
E70.1
Other hyperphenylalaninemias
2016
2017
2018
2019
2020
2021
Billable/Specific Code
phosphoenolpyruvate carboxykinase
E74.4
ICD-10-CM Diagnosis Code
E74.4
Disorders of pyruvate metabolism and gluconeogenesis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase
Type 1 Excludes
disorders of pyruvate metabolism and gluconeogenesis with anemia (
D55.-
)
Leigh's syndrome (
G31.82
)
phosphofructokinase
E74.19
ICD-10-CM Diagnosis Code
E74.19
Other disorders of fructose metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fructose-1, 6-diphosphatase deficiency
phosphomannomutuse
E74.818
ICD-10-CM Diagnosis Code
E74.818
Other disorders of glucose transport
2021 - New Code
Billable/Specific Code
Applicable To
(Familial) renal glycosuria
phosphomannose isomerase
E74.818
ICD-10-CM Diagnosis Code
E74.818
Other disorders of glucose transport
2021 - New Code
Billable/Specific Code
Applicable To
(Familial) renal glycosuria
phosphomannosyl mutase
E74.818
ICD-10-CM Diagnosis Code
E74.818
Other disorders of glucose transport
2021 - New Code
Billable/Specific Code
Applicable To
(Familial) renal glycosuria
phosphorylase kinase, liver
E74.09
ICD-10-CM Diagnosis Code
E74.09
Other glycogen storage disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency
pituitary hormone
E23.0
(isolated)
ICD-10-CM Diagnosis Code
E23.0
Hypopituitarism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fertile eunuch syndrome
Hypogonadotropic hypogonadism
Idiopathic growth hormone deficiency
Isolated deficiency of gonadotropin
Isolated deficiency of growth hormone
Isolated deficiency of pituitary hormone
Kallmann's syndrome
Lorain-Levi short stature
Necrosis of pituitary gland (postpartum)
Panhypopituitarism
Pituitary cachexia
Pituitary insufficiency NOS
Pituitary short stature
Sheehan's syndrome
Simmonds' disease
plasma thromboplastin
antecedent
D68.1
(PTA)
ICD-10-CM Diagnosis Code
D68.1
Hereditary factor XI deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
component
D67
(PTC)
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
plasminogen
E88.02
(type 1) (type 2)
ICD-10-CM Diagnosis Code
E88.02
Plasminogen deficiency
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
Dysplasminogenemia
Hypoplasminogenemia
Type 1 plasminogen deficiency
Type 2 plasminogen deficiency
Code Also
, if applicable, ligneous conjunctivitis (
H10.51
)
Use Additional
code for associated findings, such as:
hydrocephalus (
G91.4
)
otitis media (
H67.-
)
respiratory disorder related to plasminogen deficiency (
J99
)
platelet NEC
D69.1
ICD-10-CM Diagnosis Code
D69.1
Qualitative platelet defects
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bernard-Soulier [giant platelet] syndrome
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (hemorrhagic) (hereditary)
Thrombocytopathy
Type 1 Excludes
von Willebrand's disease (
D68.0
)
constitutional
D68.0
ICD-10-CM Diagnosis Code
D68.0
Von Willebrand's disease
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Angiohemophilia
Factor VIII deficiency with vascular defect
Vascular hemophilia
Type 1 Excludes
capillary fragility (hereditary) (
D69.8
)
factor VIII deficiency NOS (
D66
)
factor VIII deficiency with functional defect (
D66
)
polyglandular
E31.8
ICD-10-CM Diagnosis Code
E31.8
Other polyglandular dysfunction
2016
2017
2018
2019
2020
2021
Billable/Specific Code
autoimmune
E31.0
ICD-10-CM Diagnosis Code
E31.0
Autoimmune polyglandular failure
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Schmidt's syndrome
potassium
E87.6
(K)
ICD-10-CM Diagnosis Code
E87.6
Hypokalemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Potassium [K] deficiency
prepuce
N47.3
ICD-10-CM Diagnosis Code
N47.3
Deficient foreskin
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Male Dx
proaccelerin (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
proconvertin factor (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
protein
E46
- see also
Malnutrition
ICD-10-CM Diagnosis Code
E46
Unspecified protein-calorie malnutrition
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Malnutrition NOS
Protein-calorie imbalance NOS
Type 1 Excludes
nutritional deficiency NOS (
E63.9
)
anemia
D53.0
ICD-10-CM Diagnosis Code
D53.0
Protein deficiency anemia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Amino-acid deficiency anemia
Orotaciduric anemia
Type 1 Excludes
Lesch-Nyhan syndrome (
E79.1
)
C
D68.59
ICD-10-CM Diagnosis Code
D68.59
Other primary thrombophilia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Antithrombin III deficiency
Hypercoagulable state NOS
Primary hypercoagulable state NEC
Primary thrombophilia NEC
Protein C deficiency
Protein S deficiency
Thrombophilia NOS
S
D68.59
ICD-10-CM Diagnosis Code
D68.59
Other primary thrombophilia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Antithrombin III deficiency
Hypercoagulable state NOS
Primary hypercoagulable state NEC
Primary thrombophilia NEC
Protein C deficiency
Protein S deficiency
Thrombophilia NOS
prothrombin (congenital) (heredItary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
Prower factor
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
pseudocholinesterase
E88.09
ICD-10-CM Diagnosis Code
E88.09
Other disorders of plasma-protein metabolism, not elsewhere classified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bisalbuminemia
PTA
D68.1
(plasma thromboplastin antecedent)
ICD-10-CM Diagnosis Code
D68.1
Hereditary factor XI deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
PTC
D67
(plasma thromboplastin component)
ICD-10-CM Diagnosis Code
D67
Hereditary factor IX deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
purine nucleoside phosphorylase
D81.5
(PNP)
ICD-10-CM Diagnosis Code
D81.5
Purine nucleoside phosphorylase [PNP] deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
pyracin
E53.1
(alpha) (beta)
ICD-10-CM Diagnosis Code
E53.1
Pyridoxine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Vitamin B6 deficiency
Type 1 Excludes
pyridoxine-responsive sideroblastic anemia (
D64.3
)
pyridoxal
E53.1
ICD-10-CM Diagnosis Code
E53.1
Pyridoxine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Vitamin B6 deficiency
Type 1 Excludes
pyridoxine-responsive sideroblastic anemia (
D64.3
)
pyridoxamine
E53.1
ICD-10-CM Diagnosis Code
E53.1
Pyridoxine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Vitamin B6 deficiency
Type 1 Excludes
pyridoxine-responsive sideroblastic anemia (
D64.3
)
pyridoxine
E53.1
(derivatives)
ICD-10-CM Diagnosis Code
E53.1
Pyridoxine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Vitamin B6 deficiency
Type 1 Excludes
pyridoxine-responsive sideroblastic anemia (
D64.3
)
pyruvate
carboxylase
E74.4
ICD-10-CM Diagnosis Code
E74.4
Disorders of pyruvate metabolism and gluconeogenesis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase
Type 1 Excludes
disorders of pyruvate metabolism and gluconeogenesis with anemia (
D55.-
)
Leigh's syndrome (
G31.82
)
dehydrogenase
E74.4
ICD-10-CM Diagnosis Code
E74.4
Disorders of pyruvate metabolism and gluconeogenesis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase
Type 1 Excludes
disorders of pyruvate metabolism and gluconeogenesis with anemia (
D55.-
)
Leigh's syndrome (
G31.82
)
riboflavin
E53.0
(vitamin B2)
ICD-10-CM Diagnosis Code
E53.0
Riboflavin deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Ariboflavinosis
Vitamin B2 deficiency
salt
E87.1
ICD-10-CM Diagnosis Code
E87.1
Hypo-osmolality and hyponatremia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Sodium [Na] deficiency
Type 1 Excludes
syndrome of inappropriate secretion of antidiuretic hormone (
E22.2
)
secretion
ovary
E28.39
ICD-10-CM Diagnosis Code
E28.39
Other primary ovarian failure
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Decreased estrogen
Resistant ovary syndrome
salivary gland
K11.7
(any)
ICD-10-CM Diagnosis Code
K11.7
Disturbances of salivary secretion
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hypoptyalism
Ptyalism
Xerostomia
Type 2 Excludes
dry mouth NOS (
R68.2
)
urine
R34
ICD-10-CM Diagnosis Code
R34
Anuria and oliguria
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
anuria and oliguria complicating abortion or ectopic or molar pregnancy (
O00
-
O07
,
O08.4
)
anuria and oliguria complicating pregnancy (
O26.83-
)
anuria and oliguria complicating the puerperium (
O90.4
)
selenium
E59
(dietary)
ICD-10-CM Diagnosis Code
E59
Dietary selenium deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Keshan disease
Type 1 Excludes
sequelae of selenium deficiency (
E64.8
)
serum antitrypsin, familial
E88.01
ICD-10-CM Diagnosis Code
E88.01
Alpha-1-antitrypsin deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AAT deficiency
short stature homeobox gene (SHOX)
with
dyschondrosteosis
Q78.8
ICD-10-CM Diagnosis Code
Q78.8
Other specified osteochondrodysplasias
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
Applicable To
Osteopoikilosis
short stature
E34.3
(idiopathic)
ICD-10-CM Diagnosis Code
E34.3
Short stature due to endocrine disorder
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Constitutional short stature
Laron-type short stature
Type 1 Excludes
achondroplastic short stature (
Q77.4
)
hypochondroplastic short stature (
Q77.4
)
nutritional short stature (
E45
)
pituitary short stature (
E23.0
)
progeria (
E34.8
)
renal short stature (
N25.0
)
Russell-Silver syndrome (
Q87.19
)
short-limbed stature with immunodeficiency (
D82.2
)
short stature in specific dysmorphic syndromes - code to syndrome - see Alphabetical Index
short stature NOS (
R62.52
)
Turner's syndrome
Q96.9
ICD-10-CM Diagnosis Code
Q96.9
Turner's syndrome, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
sodium
E87.1
(Na)
ICD-10-CM Diagnosis Code
E87.1
Hypo-osmolality and hyponatremia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Sodium [Na] deficiency
Type 1 Excludes
syndrome of inappropriate secretion of antidiuretic hormone (
E22.2
)
SPCA
D68.2
(factor VII)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
sphincter, intrinsic
N36.42
ICD-10-CM Diagnosis Code
N36.42
Intrinsic sphincter deficiency (ISD)
2016
2017
2018
2019
2020
2021
Billable/Specific Code
with urethral hypermobility
N36.43
ICD-10-CM Diagnosis Code
N36.43
Combined hypermobility of urethra and intrinsic sphincter deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
stable factor (congenital) (hereditary)
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
acquired
D68.4
ICD-10-CM Diagnosis Code
D68.4
Acquired coagulation factor deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Type 1 Excludes
vitamin K deficiency of newborn (
P53
)
Stuart-Prower
D68.2
(factor X)
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
succinic semialdehyde dehydrogenase
E72.81
ICD-10-CM Diagnosis Code
E72.81
Disorders of gamma aminobutyric acid metabolism
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
4-hydroxybutyric aciduria
Disorders of GABA metabolism
GABA metabolic defect
GABA transaminase deficiency
GABA-T deficiency
Gamma-hydroxybutyric aciduria
SSADHD
Succinic semialdehyde dehydrogenase deficiency
sucrase
E74.39
ICD-10-CM Diagnosis Code
E74.39
Other disorders of intestinal carbohydrate absorption
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Disorder of intestinal carbohydrate absorption NOS
Glucose-galactose malabsorption
Sucrase deficiency
sulfatase
E75.26
ICD-10-CM Diagnosis Code
E75.26
Sulfatase deficiency
2019 - New Code
2020
2021
Billable/Specific Code
Applicable To
Multiple sulfatase deficiency (MSD)
sulfite oxidase
E72.19
ICD-10-CM Diagnosis Code
E72.19
Other disorders of sulfur-bearing amino-acid metabolism
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Cystathioninuria
Methioninemia
Sulfite oxidase deficiency
thiamin, thiaminic (chloride)
E51.9
ICD-10-CM Diagnosis Code
E51.9
Thiamine deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
beriberi (dry)
E51.11
ICD-10-CM Diagnosis Code
E51.11
Dry beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi NOS
Beriberi with polyneuropathy
wet
E51.12
ICD-10-CM Diagnosis Code
E51.12
Wet beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi with cardiovascular manifestations
Cardiovascular beriberi
Shoshin disease
thrombokinase
D68.2
ICD-10-CM Diagnosis Code
D68.2
Hereditary deficiency of other clotting factors
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
newborn
P53
ICD-10-CM Diagnosis Code
P53
Hemorrhagic disease of newborn
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code on Newborn Record
Applicable To
Vitamin K deficiency of newborn
thyroid (gland) - see
Hypothyroidism
tocopherol
E56.0
ICD-10-CM Diagnosis Code
E56.0
Deficiency of vitamin E
2016
2017
2018
2019
2020
2021
Billable/Specific Code
tooth bud
K00.0
ICD-10-CM Diagnosis Code
K00.0
Anodontia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hypodontia
Oligodontia
Type 1 Excludes
acquired absence of teeth (
K08.1-
)
transcobalamine II
D51.2
(anemia)
ICD-10-CM Diagnosis Code
D51.2
Transcobalamin II deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
vanadium
E61.6
ICD-10-CM Diagnosis Code
E61.6
Vanadium deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
vascular
I99.9
ICD-10-CM Diagnosis Code
I99.9
Unspecified disorder of circulatory system
2016
2017
2018
2019
2020
2021
Billable/Specific Code
vasopressin
E23.2
ICD-10-CM Diagnosis Code
E23.2
Diabetes insipidus
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
nephrogenic diabetes insipidus (
N25.1
)
vertical ridge
K06.8
ICD-10-CM Diagnosis Code
K06.8
Other specified disorders of gingiva and edentulous alveolar ridge
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Fibrous epulis
Flabby alveolar ridge
Giant cell epulis
Peripheral giant cell granuloma of gingiva
Pyogenic granuloma of gingiva
Vertical ridge deficiency
Type 2 Excludes
gingival cyst (
K09.0
)
viosterol - see
Deficiency, calciferol
vitamin (multiple)
E56.9
ICD-10-CM Diagnosis Code
E56.9
Vitamin deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
A
E50.9
ICD-10-CM Diagnosis Code
E50.9
Vitamin A deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Hypovitaminosis A NOS
sequelae
E64.1
ICD-10-CM Diagnosis Code
E64.1
Sequelae of vitamin A deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
with
Bitot's spot
E50.1
(corneal)
ICD-10-CM Diagnosis Code
E50.1
Vitamin A deficiency with Bitot's spot and conjunctival xerosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bitot's spot in the young child
follicular keratosis
E50.8
ICD-10-CM Diagnosis Code
E50.8
Other manifestations of vitamin A deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Follicular keratosis
Xeroderma
keratomalacia
E50.4
ICD-10-CM Diagnosis Code
E50.4
Vitamin A deficiency with keratomalacia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
manifestations NEC
E50.8
ICD-10-CM Diagnosis Code
E50.8
Other manifestations of vitamin A deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Follicular keratosis
Xeroderma
night blindness
E50.5
ICD-10-CM Diagnosis Code
E50.5
Vitamin A deficiency with night blindness
2016
2017
2018
2019
2020
2021
Billable/Specific Code
scar of cornea, xerophthalmic
E50.6
ICD-10-CM Diagnosis Code
E50.6
Vitamin A deficiency with xerophthalmic scars of cornea
2016
2017
2018
2019
2020
2021
Billable/Specific Code
xeroderma
E50.8
ICD-10-CM Diagnosis Code
E50.8
Other manifestations of vitamin A deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Follicular keratosis
Xeroderma
xerophthalmia
E50.7
ICD-10-CM Diagnosis Code
E50.7
Other ocular manifestations of vitamin A deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Xerophthalmia NOS
xerosis
conjunctival
E50.0
ICD-10-CM Diagnosis Code
E50.0
Vitamin A deficiency with conjunctival xerosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
and Bitot's spot
E50.1
ICD-10-CM Diagnosis Code
E50.1
Vitamin A deficiency with Bitot's spot and conjunctival xerosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Bitot's spot in the young child
cornea
E50.2
ICD-10-CM Diagnosis Code
E50.2
Vitamin A deficiency with corneal xerosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
and ulceration
E50.3
ICD-10-CM Diagnosis Code
E50.3
Vitamin A deficiency with corneal ulceration and xerosis
2016
2017
2018
2019
2020
2021
Billable/Specific Code
B (complex)
E53.9
ICD-10-CM Diagnosis Code
E53.9
Vitamin B deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
with
beriberi (dry)
E51.11
ICD-10-CM Diagnosis Code
E51.11
Dry beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi NOS
Beriberi with polyneuropathy
wet
E51.12
ICD-10-CM Diagnosis Code
E51.12
Wet beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi with cardiovascular manifestations
Cardiovascular beriberi
Shoshin disease
pellagra
E52
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
B1 NOS
E51.9
ICD-10-CM Diagnosis Code
E51.9
Thiamine deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
beriberi (dry)
E51.11
ICD-10-CM Diagnosis Code
E51.11
Dry beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi NOS
Beriberi with polyneuropathy
wet
E51.12
ICD-10-CM Diagnosis Code
E51.12
Wet beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi with cardiovascular manifestations
Cardiovascular beriberi
Shoshin disease
with circulatory system manifestations
E51.11
ICD-10-CM Diagnosis Code
E51.11
Dry beriberi
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Beriberi NOS
Beriberi with polyneuropathy
B12
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
B2
E53.0
(riboflavin)
ICD-10-CM Diagnosis Code
E53.0
Riboflavin deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Ariboflavinosis
Vitamin B2 deficiency
B6
E53.1
ICD-10-CM Diagnosis Code
E53.1
Pyridoxine deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Vitamin B6 deficiency
Type 1 Excludes
pyridoxine-responsive sideroblastic anemia (
D64.3
)
C
E54
ICD-10-CM Diagnosis Code
E54
Ascorbic acid deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Deficiency of vitamin C
Scurvy
Type 1 Excludes
scorbutic anemia (
D53.2
)
sequelae of vitamin C deficiency (
E64.2
)
sequelae
E64.2
ICD-10-CM Diagnosis Code
E64.2
Sequelae of vitamin C deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
POA Exempt
D
E55.9
ICD-10-CM Diagnosis Code
E55.9
Vitamin D deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Avitaminosis D
25-hydroxylase
E83.32
ICD-10-CM Diagnosis Code
E83.32
Hereditary vitamin D-dependent rickets (type 1) (type 2)
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
25-hydroxyvitamin D 1-alpha-hydroxylase deficiency
Pseudovitamin D deficiency
Vitamin D receptor defect
with
adult osteomalacia
M83.8
ICD-10-CM Diagnosis Code
M83.8
Other adult osteomalacia
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Adult Dx (15-124 years)
rickets - see
Rickets
E
E56.0
ICD-10-CM Diagnosis Code
E56.0
Deficiency of vitamin E
2016
2017
2018
2019
2020
2021
Billable/Specific Code
folic acid
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
G
E53.0
ICD-10-CM Diagnosis Code
E53.0
Riboflavin deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Ariboflavinosis
Vitamin B2 deficiency
group B
E53.9
ICD-10-CM Diagnosis Code
E53.9
Vitamin B deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
specified NEC
E53.8
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
H
E53.8
(biotin)
ICD-10-CM Diagnosis Code
E53.8
Deficiency of other specified B group vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Biotin deficiency
Cyanocobalamin deficiency
Folate deficiency
Folic acid deficiency
Pantothenic acid deficiency
Vitamin B12 deficiency
Type 1 Excludes
folate deficiency anemia (
D52.-
)
vitamin B12 deficiency anemia (
D51.-
)
K
E56.1
ICD-10-CM Diagnosis Code
E56.1
Deficiency of vitamin K
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Type 1 Excludes
deficiency of coagulation factor due to vitamin K deficiency (
D68.4
)
vitamin K deficiency of newborn (
P53
)
of newborn
P53
ICD-10-CM Diagnosis Code
P53
Hemorrhagic disease of newborn
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Code on Newborn Record
Applicable To
Vitamin K deficiency of newborn
nicotinic
E52
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
P
E56.8
ICD-10-CM Diagnosis Code
E56.8
Deficiency of other vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
PP
E52
(pellagra-preventing)
ICD-10-CM Diagnosis Code
E52
Niacin deficiency [pellagra]
2016
2017
2018
2019
2020
2021
Billable/Specific Code
Applicable To
Niacin (-tryptophan) deficiency
Nicotinamide deficiency
Pellagra (alcoholic)
Type 1 Excludes
sequelae of niacin deficiency (
E64.8
)
specified NEC
E56.8
ICD-10-CM Diagnosis Code
E56.8
Deficiency of other vitamins
2016
2017
2018
2019
2020
2021
Billable/Specific Code
thiamin
E51.9
ICD-10-CM Diagnosis Code
E51.9
Thiamine deficiency, unspecified
2016
2017
2018
2019
2020
2021
Billable/Specific Code
beriberi - see
Beriberi
zinc, dietary
E60
ICD-10-CM Diagnosis Code
E60
Dietary zinc deficiency
2016
2017
2018
2019
2020
2021
Billable/Specific Code